#METABOLOMICS WORKBENCH niw_20160202_9761381_mwtab.txt DATATRACK_ID:497 kenanazam_20160222_153248 STUDY_ID:ST000352 ANALYSIS_ID:AN000572 PROJECT_ID:PR000281 VERSION 1 CREATED_ON February 22, 2016, 5:00 pm #PROJECT PR:PROJECT_TITLE Metabolic profiling reveals biochemical pathways and potential biomarkers PR:PROJECT_TITLE associated with the pathogenesis of Krabbe disease PR:PROJECT_TYPE Disease Profiling PR:PROJECT_SUMMARY Krabbe disease (KD) is caused by mutations in the galactosylceramidase (GALC) PR:PROJECT_SUMMARY gene, which encodes a lysosomal enzyme that degrades galactolipids, including PR:PROJECT_SUMMARY galactosylceramide and galactosylsphingosine (psychosine). GALC deficiency PR:PROJECT_SUMMARY results in progressive intracellular accumulation of psychosine, which is PR:PROJECT_SUMMARY believed to be the main cause for the demyelinating neurodegeneration in KD PR:PROJECT_SUMMARY pathology. Umbilical cord blood transplantation slows disease progression if PR:PROJECT_SUMMARY performed presymptomatically, but carries a significant risk of morbidity and PR:PROJECT_SUMMARY mortality. Accurate presymptomatic diagnosis is therefore critical to facilitate PR:PROJECT_SUMMARY the efficacy of existing transplant approaches and avoid unnecessary treatment PR:PROJECT_SUMMARY of children who will not develop KD. Unfortunately current diagnostic criteria, PR:PROJECT_SUMMARY including GALC activity, genetic analysis, and psychosine measurement, are PR:PROJECT_SUMMARY insufficient for secure presymptomatic diagnosis. Herein, we performed a global PR:PROJECT_SUMMARY metabolomic analysis to identify pathogenetic metabolic pathways and novel PR:PROJECT_SUMMARY biomarkers implicated in the authentic mouse model of KD, twitcher. At a time PR:PROJECT_SUMMARY point before onset of signs of disease, twitcher hindbrains had metabolic PR:PROJECT_SUMMARY profiles similar to wild type, with the exception of a decrease in metabolites PR:PROJECT_SUMMARY related to glucose energy metabolism. Instead, many metabolic pathways were PR:PROJECT_SUMMARY altered after early signs of disease in the twitcher, including decreased PR:PROJECT_SUMMARY phospholipid turnover, restricted mitochondrial metabolism of branched-chain PR:PROJECT_SUMMARY amino acids, increased inflammation, neurotransmitter metabolism and osmolytes. PR:PROJECT_SUMMARY Hypoxanthine, a purine derivative, is increased before signs of disease appear, PR:PROJECT_SUMMARY suggesting its potential as a biomarker for early diagnosis of KD. Additionally, PR:PROJECT_SUMMARY given the early changes in glucose metabolism in the pathogenesis of KD, PR:PROJECT_SUMMARY diagnostic modalities that report metabolic function, such as positron emission PR:PROJECT_SUMMARY tomography, may be useful in KD. PR:INSTITUTE University at Buffalo PR:DEPARTMENT Hunter James Kelly Research Institute PR:LABORATORY Shin Laboratory PR:LAST_NAME Shin PR:FIRST_NAME Daesung PR:ADDRESS NYS Center of Excellence in Bioinformatics & Life Sciences, 701 Ellicott Street, PR:ADDRESS Buffalo, NY 14203 PR:EMAIL daesungs@buffalo.edu PR:PHONE 716-881-8980 #STUDY ST:STUDY_TITLE Metabolic profiling reveals biochemical pathways and potential biomarkers ST:STUDY_TITLE associated with the pathogenesis of Krabbe disease ST:STUDY_TYPE Animal hindbrain comparison ST:STUDY_SUMMARY P15 wildtype mouse hindbrains, P15 twitcher mouse hindbrains, P22 wildtype mouse ST:STUDY_SUMMARY hindbrains, P22 twitcher mouse hindbrains ST:INSTITUTE University at Buffalo ST:DEPARTMENT Hunter James Kelly Research Institute ST:LABORATORY Shin Laboratory ST:LAST_NAME Shin ST:FIRST_NAME Daesung ST:ADDRESS NYS Center of Excellence in Bioinformatics & Life Sciences, 701 Ellicott Street, ST:ADDRESS Buffalo, NY 14203 ST:EMAIL daesungs@buffalo.edu ST:PHONE 716-881-8980 ST:NUM_GROUPS 4 ST:TOTAL_SUBJECTS 32 #SUBJECT SU:SUBJECT_TYPE Animal SU:SUBJECT_SPECIES Mus musculus SU:TAXONOMY_ID 10090 SU:GENOTYPE_STRAIN C57BL/6N|C57BL/6N Twitcher SU:AGE_OR_AGE_RANGE P15-P22 days #SUBJECT_SAMPLE_FACTORS: SUBJECT(optional)[tab]SAMPLE[tab]FACTORS(NAME:VALUE pairs separated by |)[tab]Additional sample data SUBJECT_SAMPLE_FACTORS - UBUF-00091 age:P15 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00092 age:P15 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00093 age:P15 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00094 age:P15 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00095 age:P15 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00096 age:P15 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00097 age:P15 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00098 age:P15 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00099 age:P15 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00100 age:P15 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00101 age:P15 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00102 age:P15 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00103 age:P15 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00104 age:P15 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00105 age:P15 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00106 age:P15 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00107 age:P22 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00108 age:P22 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00109 age:P22 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00110 age:P22 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00111 age:P22 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00112 age:P22 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00113 age:P22 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00114 age:P22 | genotype:Wild Type SUBJECT_SAMPLE_FACTORS - UBUF-00115 age:P22 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00116 age:P22 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00117 age:P22 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00118 age:P22 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00119 age:P22 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00120 age:P22 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00121 age:P22 | genotype:Twitcher SUBJECT_SAMPLE_FACTORS - UBUF-00122 age:P22 | genotype:Twitcher #COLLECTION CO:COLLECTION_SUMMARY None CO:COLLECTION_PROTOCOL_ID COL_PROT CO:COLLECTION_PROTOCOL_FILENAME COL_PROT.pdf CO:SAMPLE_TYPE Hindbrain (pons, medulla, brainstem, cerebellum) CO:VOLUMEORAMOUNT_COLLECTED entire hindbrain #TREATMENT TR:TREATMENT_SUMMARY none #SAMPLEPREP SP:SAMPLEPREP_SUMMARY None SP:PROCESSING_METHOD Homogenization SP:PROCESSING_STORAGE_CONDITIONS On Ice SP:ORGAN Brain SP:ORGAN_SPECIFICATION Hindbrain #CHROMATOGRAPHY CH:CHROMATOGRAPHY_SUMMARY Experiments were conducted according to the protocols approved by the CH:CHROMATOGRAPHY_SUMMARY Institutional Animal Care and Use Committee of University at Buffalo and Roswell CH:CHROMATOGRAPHY_SUMMARY Park Cancer Institute. Twitcher mice were maintained on the background of CH:CHROMATOGRAPHY_SUMMARY C57BL/6N. Breeder C57BL/6N mice were purchased from Charles River. Freshly CH:CHROMATOGRAPHY_SUMMARY collected hindbrain regions from twitcher and WT littermate mice at P8, P15, CH:CHROMATOGRAPHY_SUMMARY P22, and P34 days were transferred into polypropylene cryovials, and then frozen CH:CHROMATOGRAPHY_SUMMARY in liquid nitrogen and stored at - 80°C until the analysis. CH:CHROMATOGRAPHY_TYPE UPLC CH:INSTRUMENT_NAME Waters ACQUITY UPLC CH:COLUMN_NAME See doc CH:METHODS_FILENAME Protocol.pdf #ANALYSIS AN:ANALYSIS_TYPE MS AN:ANALYSIS_PROTOCOL_FILE Protocol.pdf #MS MS:MS_COMMENTS - MS:INSTRUMENT_NAME Thermo LTQ MS:INSTRUMENT_TYPE Single quadrupole MS:MS_TYPE ESI MS:ION_MODE POSITIVE #MS_METABOLITE_DATA MS_METABOLITE_DATA:UNITS Peak height MS_METABOLITE_DATA_START Samples UBUF-00091 UBUF-00092 UBUF-00093 UBUF-00094 UBUF-00095 UBUF-00096 UBUF-00097 UBUF-00098 UBUF-00099 UBUF-00100 UBUF-00101 UBUF-00102 UBUF-00103 UBUF-00104 UBUF-00105 UBUF-00106 UBUF-00107 UBUF-00108 UBUF-00109 UBUF-00110 UBUF-00111 UBUF-00112 UBUF-00113 UBUF-00114 UBUF-00115 UBUF-00116 UBUF-00117 UBUF-00118 UBUF-00119 UBUF-00120 UBUF-00121 UBUF-00122 Factors age:P15 | genotype:Wild Type age:P15 | genotype:Wild Type age:P15 | genotype:Wild Type age:P15 | genotype:Wild Type age:P15 | genotype:Wild Type age:P15 | genotype:Wild Type age:P15 | genotype:Wild Type age:P15 | genotype:Wild Type age:P15 | genotype:Twitcher age:P15 | genotype:Twitcher age:P15 | genotype:Twitcher age:P15 | genotype:Twitcher age:P15 | genotype:Twitcher age:P15 | genotype:Twitcher age:P15 | genotype:Twitcher age:P15 | genotype:Twitcher age:P22 | genotype:Wild Type age:P22 | genotype:Wild Type age:P22 | genotype:Wild Type age:P22 | genotype:Wild Type age:P22 | genotype:Wild Type age:P22 | genotype:Wild Type age:P22 | genotype:Wild Type age:P22 | genotype:Wild Type age:P22 | genotype:Twitcher age:P22 | genotype:Twitcher age:P22 | genotype:Twitcher age:P22 | genotype:Twitcher age:P22 | genotype:Twitcher age:P22 | genotype:Twitcher age:P22 | genotype:Twitcher age:P22 | genotype:Twitcher 1-methylimidazoleacetate 63071 56864 73749 75039 55805 57231 63341 57953 63537 75828 70329 41998 47635 63587 52192 96778 58555 99404 51301 149467 82814 56383 116355 66249 79992 82170 70010 86805 108795 97779 65780 64813 1-oleoylglycerophosphocholine (18:1) 247944 131378 95203 62890 168344 120544 107223 258948 183474 131393 197058 123444 276807 150172 63322 242701 427884 158291 565361 79346 113116 97161 416092 396204 439529 140296 106300 328036 139411 154980 81658 101240 1-palmitoleoylglycerophosphocholine (16:1)* 41544 29666 N 37115 N 37048 29876 28845 25189 40619 33916 67380 32320 36224 N 78437 56338 N 38171 15808 21893 N 28019 40997 54715 N N N N N N N 1-palmitoylglycerophosphocholine (16:0) 759719 362038 228249 169421 327099 351404 269698 988904 544516 274958 443457 376365 896879 458116 115359 775761 1463622 382488 1518605 185902 261398 268305 1155167 966461 1335968 221132 292733 1109021 365426 407369 202189 185787 1-stearoylglycerophosphocholine (18:0) 389610 101730 102122 40868 101815 74698 118604 356706 244067 34775 172297 97174 235027 65624 52315 322616 356699 74721 708432 95038 85952 71731 654568 326775 700715 90511 114509 318597 103019 164954 93599 46132 1-stearoylglycerophosphoethanolamine 182199 46287 48728 26652 58256 50550 46384 198836 151511 18509 102789 84316 144068 29381 20985 156986 172710 33342 294763 39860 46492 35047 313755 168339 301894 55672 68120 160689 51165 105602 28541 N 2-arachidonoylglycerophosphocholine* 88986 36900 36541 44639 37660 31980 31315 102877 66828 59603 51744 61585 63417 69147 38786 110257 147728 42978 150828 32851 29829 34720 88530 113671 220535 40756 47377 70458 32882 46667 59818 36186 2-arachidonoylglycerophosphoethanolamine* 831608 487781 357551 198752 436812 398260 431988 1015309 583990 344806 659500 421076 729165 389776 210985 903080 1338234 525102 1742229 453352 388994 453160 1039025 1040703 1485894 359036 405385 1002543 492211 355613 483710 257010 2-docosahexaenoylglycerophosphocholine* 58777 55527 41294 N N 30223 23705 93085 54481 21022 37740 19336 74101 40495 33029 97304 112428 42349 143731 N 28013 34280 131023 98619 155561 46987 47153 116622 30957 39655 35786 43995 2-docosahexaenoylglycerophosphoethanolamine* 1402750 792009 781590 385780 699462 576633 690107 1772658 875306 568237 1189317 594423 1084807 738706 342618 1566773 2272328 831518 2925357 658510 551697 700135 2050375 1726168 2526755 544416 900112 1806240 753492 799830 767779 427716 2-docosapentaenoylglycerophosphoethanolamine* 65117 N 52114 28704 46788 37791 43027 65571 57865 20943 N N 77839 41658 36003 73552 84794 34683 129473 26723 N 37344 94274 71850 127861 30438 38632 78799 46018 43788 48481 28010 2-linoleoylglycerophosphoethanolamine* 59772 N 35760 N N N 49003 57608 N N 42177 38248 37777 N 28286 46897 88471 32319 108814 58565 39332 N 71944 52729 67066 19518 31832 58571 26164 32069 30294 N 2-methylbutyrylcarnitine (C5) 33281 57431 77862 46097 64534 42732 68550 84581 67592 80660 59484 51057 43097 63480 81045 102138 79501 41604 41839 36875 36192 68473 65623 56471 61527 55445 51086 64833 76505 73708 82329 108763 2-oleoylglycerophosphocholine* 144635 232793 277884 359655 113699 150743 169749 232639 267414 188650 163968 139913 217364 238123 153734 218730 371133 272866 402927 N 199730 269536 433042 361030 491114 174065 205705 376176 260040 107313 N 161275 2-palmitoylglycerophosphocholine* 166451 78018 56238 49545 77329 60798 49718 193592 128861 59063 157129 56151 182701 84466 37164 209905 360222 80519 395695 70141 62889 60320 251412 203200 383469 43041 51989 235172 89574 93635 61777 56703 2-palmitoylglycerophosphoethanolamine* 71144 55494 31728 N 38713 52585 51262 113414 53345 27295 103359 45668 80473 37102 N 142918 176808 42441 223472 36973 45584 44489 178530 120943 220196 54916 52179 132010 65029 56107 22652 47972 3-dehydrocarnitine* 1110388 1102523 1212170 915143 1331912 889384 883248 908953 1206755 947701 1197288 766126 890549 880850 983638 995527 1409224 1096397 1321417 1008780 1034060 1006547 1135586 1014622 1831814 1249224 1966765 1193936 1338209 1291817 1405356 1281767 4-guanidinobutanoate 374836 430736 430585 478333 295620 393232 434186 415276 380026 366504 409114 316037 336078 334316 411896 365320 292379 474198 329693 429745 360131 459787 484192 364205 215143 357238 332071 298048 328920 328005 316264 289130 5-aminovalerate 1131956 985757 810035 935057 754542 925041 756707 1168908 1082276 907220 882803 1191536 1083131 933753 922402 1001354 873665 793386 768695 492984 795879 601039 689641 584488 666029 732508 689570 775032 613624 789560 725110 661049 5-methylthioadenosine (MTA) 176847 198803 181533 181452 215856 226449 173710 179141 239616 172025 167663 211188 224840 187448 179530 179400 126912 159654 125256 141093 142398 107705 158110 104240 131191 164391 156287 153644 134552 112072 134218 115802 acetylcarnitine 1927649 1749282 2158514 2217970 2323355 1690564 2055082 2139041 1849622 2119466 2233485 2125415 1989064 1966415 2313564 2237199 2494275 2449912 1823948 2151724 2041911 1849308 1986906 1873194 3229711 2187827 2712717 3040958 2673960 2678528 2760627 2784029 adenosine 296986 399690 365061 295313 186262 204557 412360 382503 248891 311647 366468 285236 286097 258556 343030 383553 557023 1062835 8709224 12865831 5137464 3590686 1149415 1471347 478204 521393 3914808 599043 922226 387140 522178 511711 adenosine 2'-monophosphate (2'-AMP) 82387 85426 95518 88632 71330 80416 88176 88209 99273 98998 80871 43092 96400 69585 72405 112176 79195 89244 50903 56119 61668 60592 97162 67502 83059 76528 91270 67500 103365 66350 98573 85277 adenosine 5'-monophosphate (AMP) 458754 495663 606089 449920 513248 515424 564334 460895 451203 499509 549923 426025 447059 501442 522043 601648 516333 597830 466340 606610 548482 552048 594187 596644 551848 526918 648970 510425 695439 450634 541675 478768 arginine 1281255 1351440 1368070 1434391 1055859 1406723 1414569 1473822 1389281 1389771 1424472 1359864 1428689 1411515 1434236 1399140 1450813 1451299 1251625 1549201 1275862 1474222 1685284 1594854 1543370 1494205 1375627 1452941 1522147 1463500 1515883 1463937 argininosuccinate 209050 222630 199975 198865 225814 196539 215164 231116 194042 212615 207407 240249 230324 195099 241551 235722 265768 226045 209141 N 234070 270341 331284 244956 272463 267466 235290 242760 253429 232268 291735 266458 beta-hydroxyisovaleroylcarnitine 110598 82538 115495 102967 128901 113372 127540 136932 102868 121238 121777 80398 106615 119241 97997 122005 169464 138031 163911 191269 160966 153334 202511 134761 234864 176702 210420 193742 159578 209097 196251 167197 betaine 509701 491974 435058 599893 572406 596888 503113 456896 632419 500132 426566 540031 528892 591667 496633 516266 484684 518180 480123 723155 465631 531069 557670 624580 359325 318394 400239 416253 390033 376671 478769 427160 butyrylcarnitine 45615 48816 64985 58336 45793 44967 70530 56608 37350 47569 82776 40958 54799 51093 37569 84195 54251 64972 36015 45727 64922 46531 47461 66933 66959 52234 72474 68847 100666 70154 108657 82368 carnitine 2225302 2563028 2434014 2278514 3456039 2527100 3027879 2833837 2752801 2264706 2807534 1996520 2328566 2357980 3090152 3046594 3899932 3653665 3465693 3549596 3591709 3711672 3822665 3733973 4856271 3887153 4694849 4665190 4218015 4415202 4692722 4422227 C-glycosyltryptophan* 214158 178594 254272 196250 209677 201688 223852 220550 224255 205678 200220 169768 190698 182211 205305 211824 184515 203176 175995 177909 192843 157626 241075 179464 188228 188520 163970 156780 184074 177407 197426 168048 choline 26774472 30385030 28881230 26392696 26003672 26108048 29375362 29106958 27447646 25814794 28228188 25721940 27166168 26848710 29715608 29839330 35405296 34304264 31760910 34526780 32651814 33299510 36503796 33771128 36301520 36027656 33035264 35433192 35787212 34309208 34492912 30987408 choline phosphate 4436355 4369742 3385686 4577534 4352826 4867791 3675724 3971255 5484038 4320085 3548954 4752344 4735099 4504493 3973662 3916097 2516533 2845016 2857324 2660980 2681267 2409746 2519257 2432723 2584338 2558751 2740741 2689842 2532916 2186208 2127298 2226095 citrulline 227701 267341 242097 283200 207031 278289 252234 235364 287755 269100 257894 231086 257466 280161 251710 237160 272229 255055 212987 190580 209217 232909 252278 233129 213172 175933 187741 213498 191143 202745 192528 170853 corticosterone N N 28300 N N N 18681 22282 25682 19105 20742 N N N N N N 42200 32670 33752 65511 51870 42138 45146 51809 71203 67117 50190 55867 93052 82456 54762 creatine 110357424 106463416 104550112 112325752 119670864 111841384 99001824 100768656 99417576 109323384 112142032 108207312 101005584 112140384 103008792 120204560 104814816 114559608 98565296 100798768 113190784 117571840 123895256 105289720 108815888 108185504 102092032 110978768 118444816 114754088 104823048 127229856 creatinine 338571 309710 369255 301838 251987 293187 386029 386282 320857 331889 327639 307253 286006 348413 364112 320760 366245 408193 349972 359302 375430 364399 342996 303458 338974 274365 433620 287322 364110 315715 300211 321532 cysteine-glutathione disulfide 322719 301834 298241 315102 240872 343620 278673 384723 407163 333681 330959 247300 368631 309096 444706 349049 509475 561842 451042 373169 496229 406808 519739 432824 523159 451313 399065 602450 386076 551133 499876 416806 cytidine 1100284 845177 733566 865178 1191106 1286453 714156 920349 1204582 886171 770515 989974 950143 814584 902160 735792 784283 847400 796061 483334 763019 526818 606163 518382 632947 620932 573957 824797 594290 651893 491120 519252 cytidine 5'-diphosphocholine 225498 205452 228227 243389 70721 94506 208610 216777 210810 221273 216119 233376 234699 243932 216371 245220 165858 180862 174577 202040 187648 177736 203427 200789 178392 187474 167367 201303 154504 187965 178078 156526 cytidine 5'-monophosphate (5'-CMP) 187984 180695 195143 156550 235324 243457 183247 196988 195442 152425 140167 159017 195445 188465 183179 195928 158195 134764 141699 142001 155490 127747 131046 138187 134547 145653 148027 142253 118873 131114 138782 129382 cytidine-5'-diphosphoethanolamine 113462 164829 158560 194326 272740 242721 132553 137558 155197 164368 142656 150468 165568 144376 134927 143357 115011 101106 100036 121834 76997 109628 101280 123247 119207 96996 93361 117298 134459 115323 105846 79129 deoxycarnitine 161502 156185 127768 172373 116628 178264 136450 169408 157815 158110 130898 162215 163020 137837 153636 120842 140109 207196 178095 160933 171799 133095 137273 166447 N 141005 155077 138504 126916 116706 106346 122575 dimethylarginine (SDMA + ADMA) 35126 48614 43792 67327 53412 39247 26909 30785 37040 38453 28998 29483 N 43306 18879 39996 20101 49231 N 23719 35286 33008 30496 27520 26304 45509 45221 28820 30792 55056 30215 41895 ergothioneine 36196 41279 34936 31234 14888 44270 77632 57677 56718 54460 48895 37953 48093 N 68964 56765 59237 40641 34149 61187 21920 52206 59113 71269 29530 35207 73215 63876 45495 40321 87899 53165 gamma-glutamylglutamate 842311 771035 746488 583121 696771 787890 773534 918363 974646 724264 790211 663599 706540 580342 1049319 880404 1345644 1318216 1281502 1203554 1300631 1038832 1355928 1024274 1250232 1379231 1174407 1385468 1167398 1121110 1026528 997705 gamma-glutamylglutamine 237693 273569 319116 247788 294547 269637 274364 272551 273558 299083 300650 188820 287857 235828 274953 254532 285471 368186 292896 323706 328055 317812 364817 313606 320104 284437 329318 309319 312432 302611 308196 313721 gamma-glutamylleucine 38689 43578 62974 40060 34098 44899 34854 50436 62746 39117 40312 36774 48145 49666 51353 47169 28279 38223 28302 24245 33231 36862 44611 31063 38374 56821 34425 42088 33528 55041 48358 45390 gamma-glutamylphenylalanine 35219 35898 19974 N 23180 49982 32916 32646 52105 35891 N 35983 29832 30521 28372 39498 36492 29303 44558 22190 28455 23045 19146 24300 49227 39548 33848 45998 24783 40412 31752 30263 gamma-glutamylthreonine* 29190 30873 32002 37106 26183 34411 24598 42722 41611 34190 22332 36046 37141 48121 42924 41539 16776 21072 15395 21778 N N 23122 N 33362 25363 21384 22750 25218 17229 23873 18872 gamma-glutamyltyrosine 33963 27860 26628 23082 15145 26975 25682 30995 32247 17021 20846 27625 49001 24093 28650 28096 23953 19008 18724 18389 21377 25207 32472 13939 26961 32469 20260 33901 28490 27625 26333 20249 glutamate 11958805 11827720 11553454 10372184 9572741 11080527 12864618 12725684 12737107 12025172 11808039 9888966 10889636 10551615 13467109 12681519 14483922 16302022 15859292 15213586 14672591 13456672 13642680 13544358 14229805 14436261 15915244 14451938 14565391 12507543 12469822 13305641 glutamate, gamma-methyl ester 83453 79904 95458 74853 96062 121587 99175 111313 119718 88816 71091 56931 128517 68010 70506 110955 87737 101898 83425 88360 100909 71991 113767 73475 84367 53317 85864 86839 74140 77059 57541 49009 glutamine 21914802 23780414 24111034 22222872 24358260 23780294 20875054 21191768 24472572 24232042 23098810 22546598 24001480 23422408 19773326 21019344 20694308 22785886 22142268 22143446 22987928 22107342 22923474 21428254 21612250 22195436 23170510 23160862 23448586 21086572 21150744 22215962 glutathione, oxidized (GSSG) 2630199 2580607 2350853 2891270 2462186 2853099 2482523 2769265 2592886 2679764 2445792 2863417 3232693 2691328 2772670 2585635 2746901 2967669 2325943 2388703 2736865 2593344 2947943 2557652 2480819 2448222 2576325 2768408 2674122 2442967 2586900 2347529 glutathione, reduced (GSH) 1139473 1367006 1925677 1139572 1435026 1511333 1976013 1461596 1737061 1842330 1596206 689763 1007666 1132587 1283755 2112842 685104 1248047 783329 2914948 1075759 2145059 2028830 1955873 1300362 1973653 2157363 731304 2588700 1104243 1823749 1736386 glycerophosphorylcholine (GPC) 1525705 1514669 1891788 1084815 658352 546513 1527716 1512497 1195320 1933453 2214324 662834 1113434 1082898 1033961 1326388 1716534 3535467 3221036 4086658 2866301 3418174 3409085 3401061 1485940 2333732 3379565 2222248 3420448 1310681 2500722 2363304 glycylleucine 47766 27237 37833 32113 29881 45786 54831 26802 28197 41107 79441 15500 36627 67455 37070 65886 32358 54633 35398 47195 56227 51418 42696 61451 61153 41742 47984 70942 49479 31803 48303 70309 guanosine 992822 1106619 1051687 1505275 1429879 1507698 1092572 1007203 1186353 1313597 1041583 1150116 1212162 1272031 1011407 894560 873271 1081423 630155 743078 1017966 919471 704302 735643 743943 563327 696557 643033 763501 606394 618138 757755 guanosine 5'- monophosphate (5'-GMP) 40632 30449 36906 42040 131591 99499 45592 22349 46563 49252 47121 32012 38359 48655 46058 45119 27863 25661 29683 29849 33890 21576 37747 30947 37383 N 22399 20160 25933 23068 23870 20791 homocitrulline 71142 43579 44598 44199 96926 88098 82495 68598 49721 45505 55111 62051 52404 65510 53720 58807 97883 83867 78438 57342 65250 107116 96243 113561 80957 65855 84391 74198 63739 84768 104526 84520 hydroxybutyrylcarnitine* 88426 96565 209921 145444 109994 98546 188941 161974 59276 149384 183784 114893 114295 99537 157022 257188 109695 47931 31435 39180 33517 36948 36606 48826 253444 82322 80588 58186 42048 164514 121099 123891 isobutyrylcarnitine 58770 48613 62782 23801 54857 61149 98575 82857 64629 75944 66015 29107 33429 46136 94854 121743 59192 50629 32846 38203 52335 49340 63640 36707 74401 62839 72882 75498 95814 85810 82327 113433 isoleucine 7059200 7460504 7757717 8547797 6952302 8810829 7358672 7894659 8442056 8871788 7737152 8260685 9310690 8682817 7418413 8174281 6415465 6543209 5041016 5660343 5640866 6062403 7853468 6256093 7550352 7064461 6456211 7391346 7517470 7453471 7798327 7352852 isovalerylcarnitine 55815 97267 109203 33065 91914 76245 68857 69005 114351 103195 65962 23705 33497 41373 85049 141405 106168 100859 81315 98789 102439 80792 109571 67309 65526 103530 116622 121137 121594 88109 125153 115096 leucine 10487952 11468685 12513483 11504374 11514268 13187874 10819267 10932142 12868002 13182857 12383314 10921124 12485704 12474798 10944886 12379021 10312417 11019605 8343901 10368146 8862560 10684820 13138461 10856204 12596714 12131284 12376660 11763843 12462127 12341876 13137182 12425319 lysine 1390155 1361526 1259823 1128860 1023292 1468638 1169236 1155205 1434100 1332282 1113389 1184414 1280062 1162789 1128921 1146009 972577 1287801 1167022 945778 1014407 944884 1042483 1127909 1145437 1213707 1085117 964816 1020917 1077908 1150510 908593 methionine 3232650 3241559 2949849 3203637 2400177 3438685 3030301 2828441 3762884 2975939 2764830 2972613 3371031 3158506 3151462 3170201 2483336 3573516 2598627 3466715 2714788 2530947 3621184 2950027 3046279 3123277 3268995 3583157 3342639 2693862 3125374 2594237 N1-methyladenosine 35641 37780 34192 43205 22626 38994 21760 24243 18020 27472 26463 40800 33168 27373 31615 25998 30154 42293 20125 21597 26623 32813 36520 27728 18972 20109 22107 17618 23101 25360 21659 N N6-acetyllysine 64048 58726 49324 45810 39115 52803 69653 59650 77090 61734 51897 44060 44451 56565 46749 72632 54322 80473 73460 57544 61978 45376 63418 61839 62456 65492 58121 47436 54093 52971 57275 67933 N6-methyladenosine 22507 28088 25549 19141 40926 25239 33769 36631 31811 17927 27490 22897 28271 30972 26534 27723 30139 32599 32500 26691 27668 22687 23499 N 30135 23491 40924 33192 32246 27715 33372 29328 N-acetyl-aspartyl-glutamate (NAAG) 2468135 2841240 2960797 2763675 2891808 3275912 2581900 2485144 2954408 3009869 2718662 2715435 2720575 2956392 2677959 3023371 2516019 2187319 2336563 2470231 2148701 2249434 2668543 2582534 2876557 2542491 2495641 2429888 2499070 2483214 2502172 2285087 N-acetylglutamate 155703 169002 182428 161671 165181 213184 210952 203433 108895 163796 173773 178901 159451 135673 197795 177418 212162 242435 199719 255456 202076 217330 238807 207159 203121 224603 195644 242169 188010 190436 250753 213887 N-acetylglutamine 107819 107269 85848 88797 95381 84094 104802 106128 117463 97505 84641 84358 81862 92294 100686 95909 139002 159954 138982 118241 137526 120879 141942 119100 127465 124860 133874 150210 127196 115097 126355 120286 N-acetylneuraminate 729618 822375 805940 780879 786911 886517 782810 823339 844610 709132 687062 663049 772629 764099 734038 936416 804762 844198 650389 672490 715620 729706 825522 698058 732705 740077 672020 745933 504793 778144 804002 690017 N-delta-acetylornithine* 38650 17685 62635 26723 114769 42314 32381 42588 54835 69344 28311 51840 47351 67772 56632 74155 182223 183874 211670 179158 197245 270104 243627 208769 81327 134118 111584 198625 196499 181699 221623 173566 nicotinamide 9819046 9881023 10611096 9576654 10516149 8908882 10827869 10807663 9997930 10336857 10308812 9101688 10464069 9313617 10564585 9789296 9862721 11600490 10522508 11531230 10503584 9928567 12408633 10290073 10785723 9569551 10840818 10730091 10887981 8868399 11205812 10689421 nicotinamide adenine dinucleotide (NAD+) N 6745 5328 N 9626 10517 N 9797 6173 7370 N 10655 N N 9949 N 14320 N 8770 7732 12428 11707 9619 10035 11724 3195 12280 8250 13448 N N 7090 ophthalmate 64494 63476 50416 85232 49391 73942 63114 59899 78424 61884 42061 81396 82963 73832 66840 61571 21997 26167 28151 16682 28422 15595 24913 29425 33349 35773 26503 20153 21541 26113 21277 26060 palmitoylcarnitine 50892 N 49364 N 44420 64139 N 42351 35559 36326 N N 47415 N N 96265 64077 22540 116821 26998 N 26461 77317 75174 125980 N 32840 44763 N N N 23898 pantothenate 1315622 1324874 1429962 1555733 1732811 1754495 1372356 1392687 1466318 1398198 1309171 1664467 1472816 1583161 1472289 1477410 1366689 1095594 1137850 1064382 1037186 1084990 1241659 1190462 1611388 1123029 1389710 1218030 1184410 1257904 1280149 1149859 phenylalanine 10023985 10747606 10631779 10245830 7906138 10777401 9674017 10179090 12353008 11146528 10015162 9742410 10434273 10114133 10654890 11478207 9223889 9594621 7430766 9332606 8221784 8906717 11302014 9941449 11519578 11961155 10800829 11252829 10949119 11606056 11543021 10899985 phosphopantetheine 30881 18289 28374 N 19759 24431 40676 31744 36506 23071 31119 23923 17751 20337 27779 32083 21673 26931 N 30736 25098 29026 30471 31639 18822 24785 30130 17325 39854 15203 29413 29428 pipecolate 287494 319246 242453 411081 746318 448296 283166 243294 368642 294480 287565 427517 369370 361749 298356 268037 253107 272198 262549 292271 267260 196865 238420 301205 198474 260470 176691 219793 284020 210140 253760 247709 pro-hydroxy-pro 54031 76840 66097 75674 53197 71561 60632 71438 53559 59697 56840 81951 84508 81733 54103 78177 33176 25901 16049 N 15434 N 16719 24868 40952 31371 11747 22290 17255 26779 31876 42392 proline 6737254 7587001 6540557 7415182 7391935 9416735 6129174 6469196 7884953 6909157 5701392 6940204 7605765 7301515 6658517 7211189 4864283 5662292 4286177 4390890 4902133 4952195 6287597 5427403 5599236 5684319 4950346 5563676 5539623 5628278 5996809 5454155 propionylcarnitine 226978 212800 141209 203836 147888 142474 253305 275984 144434 160472 220136 159006 208606 162780 277171 286805 355745 395138 289607 266587 329579 285241 339530 354961 411559 356491 395988 436847 397539 475662 466772 416459 pyridoxal 172842 152966 176884 271096 88105 167465 195830 191540 182328 123740 196480 164542 160645 210445 167526 251575 174122 168995 202046 254180 227034 140505 175276 179207 192215 143460 164995 154880 195927 137184 145747 151830 pyroglutamine* 59509 64173 85529 97553 121453 96503 43714 62100 73837 94318 99663 98198 49095 102870 33800 86566 157471 173662 193730 263437 160320 158487 159802 155708 126149 110663 146831 184758 128693 135412 105430 126760 riboflavin (Vitamin B2) 40459 33557 34883 35846 24478 24770 30604 42603 37631 30507 35341 34796 36831 33884 44457 44994 51724 35151 27221 30151 37422 33618 45716 37728 57572 38298 41088 33838 30210 50472 45512 40315 serylleucine 22009 18033 53212 27721 46995 29665 22748 N N 29758 17544 33922 N 59355 15917 N N 67935 25438 46577 33636 28593 56816 37272 58216 N 66197 N 47534 N 66619 46284 serylphenyalanine N 25718 34310 N N N 32469 N N 25172 39453 N 17649 24951 25139 27350 20741 33388 27179 25483 30002 33321 42981 34301 39236 38497 30460 21235 27444 32839 31255 45280 spermidine 1745805 2225729 1969682 1869400 2535731 2768180 1974350 2005351 2384098 2045268 1731911 2560689 2166013 1922027 1682165 2078160 1533754 1508576 1162741 1051869 1466164 1266806 1784159 1270140 1569946 1294829 1242055 1636328 1422641 1520448 1267923 1238009 spermine 279594 409354 336477 274496 558779 591380 354180 311730 452248 339066 223037 547924 374883 345669 205843 309087 180411 204838 98348 56936 207117 81612 185393 73467 162448 107312 115562 237266 109506 170202 62850 92457 stachydrine 15076 N 30778 N 17582 29011 N N N 19909 N 20720 13835 18570 26116 N 53857 61500 50885 67716 41550 50399 59667 65689 26836 48512 38895 49904 53336 49713 68857 50256 succinylcarnitine N 16237 9565 13093 31778 19387 N N 24477 14301 N 16300 N N N N 23127 17444 21334 24762 20340 20349 20240 31856 23681 16693 N 25275 N 27314 32388 31614 threonine 1761599 2018455 1866657 1847434 1317420 2033015 1902776 1931834 2235555 2244035 1693425 1792813 1990238 1958731 2138139 1903357 799034 856678 691383 914784 656779 537830 831135 696943 1623601 1103127 1306912 1123783 1040060 920825 925617 930125 tryptophan 3436297 3414326 3063751 3946895 2478488 3425300 3215324 3884073 4139262 3303226 2760447 3478617 4156675 3689253 3490047 3324229 3141589 2665035 2045131 2676784 2340259 2660376 3162175 3107398 3912399 3781780 3723711 2950070 3085251 3253720 3467624 3003904 tyrosine 5300925 5532973 4086613 5889222 3568148 6169120 5133111 5345177 5779912 4532977 3665227 6090808 6277768 6182233 5864760 5278990 4485957 4677283 3750347 4038151 4377417 4371997 5569104 4114173 4909886 5098248 4401084 5076734 5036429 4175008 4350257 4151714 valine 6744981 8234932 7226146 8398956 6580244 8505041 6688670 7077802 8340705 9092425 6737631 8689674 8757435 8929151 8075939 6866508 5363444 5437380 4243507 4720079 4672286 5397929 6543629 5578794 7599359 6644929 5912734 6172115 6590236 6813944 6549417 6458857 xanthine 2679967 2707122 2397626 2332822 2176850 2359393 2231024 2700305 2587400 2508159 2209147 2576165 2664635 2421608 2433276 2562325 2619760 2683748 2490850 2419907 2303421 2300348 2744312 2345261 2601259 2702406 2468794 2792423 2767104 2539359 2520628 2463359 xanthosine N 21647 N 24409 N N 17439 26074 15945 15995 N 30715 19477 20355 20620 20134 24872 27097 N N 24782 26911 18821 26672 21933 N 20735 19174 26746 22917 25418 30499 MS_METABOLITE_DATA_END #METABOLITES METABOLITES_START metabolite_name retention index quantified m/z PubChem ID KEGG ID 1-methylimidazoleacetate 845 141.1 75810 C05828 1-oleoylglycerophosphocholine (18:1) 5700 522.4 16081932 1-palmitoleoylglycerophosphocholine (16:1)* 5524 494.3 24779461 1-palmitoylglycerophosphocholine (16:0) 5671 496.4 86554 1-stearoylglycerophosphocholine (18:0) 5844 524.4 497299 1-stearoylglycerophosphoethanolamine 5842 482.3 9547068 2-arachidonoylglycerophosphocholine* 5524 544.3 2-arachidonoylglycerophosphoethanolamine* 5525 502.3 2-docosahexaenoylglycerophosphocholine* 5507 568.3 2-docosahexaenoylglycerophosphoethanolamine* 5512 526.2 2-docosapentaenoylglycerophosphoethanolamine* 5548 528.2 2-linoleoylglycerophosphoethanolamine* 5541 478.3 2-methylbutyrylcarnitine (C5) 2439 246.1 6426901 2-oleoylglycerophosphocholine* 5640 522.4 2-palmitoylglycerophosphocholine* 5604 496.3 15061532 2-palmitoylglycerophosphoethanolamine* 5598 454.2 3-dehydrocarnitine* 1020 160.2 6991982 C02636 4-guanidinobutanoate 1085 146.1 500 C01035 5-aminovalerate 860 118.1 138 C00431 5-methylthioadenosine (MTA) 2427 298.1 439176 C00170 acetylcarnitine 1203 204.2 1 C02571 adenosine 1650 268.1 60961 C00212 adenosine 2'-monophosphate (2'-AMP) 1625 348.1 94136 C00946 adenosine 5'-monophosphate (AMP) 1210 348.1 6083 C00020 arginine 650 175.2 232 C00062 argininosuccinate 689 291.2 16950;828 C03406 beta-hydroxyisovaleroylcarnitine 1683 262.1 betaine 721 118.2 247 C00719 butyrylcarnitine 2007 232.2 439829 C02862 carnitine 702 162.2 10917 C00318 C-glycosyltryptophan* 1912 367.1 choline 674 104.2 305 C00114 choline phosphate 695 184.1 1014 C00588 citrulline 715 176.1 9750 C00327 corticosterone 4856 347.2 5753 C02140 creatine 758 132.1 586 C00300 creatinine 730 114.1 588 C00791 cysteine-glutathione disulfide 821 427.1 4247235 cytidine 1065 244 6175 C00475 cytidine 5'-diphosphocholine 777 489.1 13804 C00307 cytidine 5'-monophosphate (5'-CMP) 887 324 6131 C00055 cytidine-5'-diphosphoethanolamine 765 447 123727 C00570 deoxycarnitine 759 146.1 134 C01181 dimethylarginine (SDMA + ADMA) 812 203.2 123831 C03626 ergothioneine 847 230.2 3032311 C05570 gamma-glutamylglutamate 1036 277.1 92865 C05282 gamma-glutamylglutamine 806 276.1 150914 C05283 gamma-glutamylleucine 2744 261.2 151023 gamma-glutamylphenylalanine 2846 295.1 111299 gamma-glutamylthreonine* 977 249.1 gamma-glutamyltyrosine 2073 311.2 94340 glutamate 700 148.1 611 C00025 glutamate, gamma-methyl ester 1062 162.1 68662 glutamine 684 147.2 5961 C00064 glutathione, oxidized (GSSG) 1535 613.1 65359 C00127 glutathione, reduced (GSH) 1274 308.1 124886 C00051 glycerophosphorylcholine (GPC) 694 258.1 71920 C00670 glycylleucine 2236 189.1 92843 C02155 guanosine 1676 284 6802 C00387 guanosine 5'- monophosphate (5'-GMP) 1300 364 6804 C00144 homocitrulline 832 190.1 65072 C02427 hydroxybutyrylcarnitine* 1475 248.2 53481617 isobutyrylcarnitine 1941 232.2 168379 isoleucine 1614 132.1 6306 C00407 isovalerylcarnitine 2533 246.2 6426851 leucine 1674 132.2 6106 C00123 lysine 603 147.2 5962 C00047 methionine 1252 150.1 6137 C00073 N1-methyladenosine 1356 282.1 27476 C02494 N6-acetyllysine 1134 189.1 92832 C02727 N6-methyladenosine 1985 282.1 102175 N-acetyl-aspartyl-glutamate (NAAG) 1563 305 5255 C12270 N-acetylglutamate 1492 190.1 70914 C00624 N-acetylglutamine 1204 189.1 182230 C02716 N-acetylneuraminate 787 310 439197 C00270 N-delta-acetylornithine* 836.2 175.1 9920500 nicotinamide 1267 123.1 936 C00153 nicotinamide adenine dinucleotide (NAD+) 1370 664 5893 C00003 ophthalmate 1457 290.1 7018721 palmitoylcarnitine 5179 400.4 461 C02990 pantothenate 2218 220.1 6613 C00864 phenylalanine 2056 166.1 6140 C00079 phosphopantetheine 2323 359.1 987 C01134 pipecolate 1120 130.1 849 C00408 pro-hydroxy-pro 960 229.2 11673055 proline 796 116.1 145742 C00148 propionylcarnitine 1589 218.2 107738 C03017 pyridoxal 1210 168.1 1050 C00250 pyroglutamine* 764 129.2 134508 riboflavin (Vitamin B2) 3111 377.2 493570 C00255 serylleucine 2106 219.2 7015695 serylphenyalanine 2348 253.2 spermidine 533 146.2 1102 C00315 spermine 506 203.2 1103 C00750 stachydrine 860 144.1 115244 C10172 succinylcarnitine 1401 262.1 threonine 713 120.1 6288 C00188 tryptophan 2445 205.1 6305 C00078 tyrosine 1516 182.1 6057 C00082 valine 1040 118.1 6287 C00183 xanthine 1430 153.1 1188 C00385 xanthosine 1785 285 64959 C01762 METABOLITES_END #END