{
"METABOLOMICS WORKBENCH":{"STUDY_ID":"ST001077","ANALYSIS_ID":"AN001759","VERSION":"1","CREATED_ON":"October 24, 2018, 2:13 pm"},

"PROJECT":{"PROJECT_TITLE":"Multi-platform metabolomics data from Ndufs4-/- skeletal muscles","PROJECT_TYPE":"Multi-platform metabolomics study","PROJECT_SUMMARY":"Multi-platform metabolomics analysis of white quadriceps and soleus skeletal muscles from the Ndufs4 knockout (Ndufs4-/-) mouse model of human Leigh syndrome.","INSTITUTE":"North-West University","LAST_NAME":"Louw","FIRST_NAME":"Roan","ADDRESS":"Hofman Street","EMAIL":"Roan.Louw@nwu.ac.za","PHONE":"+27 18 299 4074"},

"STUDY":{"STUDY_TITLE":"Multi-platform metabolomics data from Ndufs4-/- skeletal muscles (part-II)","STUDY_TYPE":"Targeted LC-MS/MS of Ndufs4-/- soleus muscles","STUDY_SUMMARY":"Targeted analysis of amino acids and acylcarnitines in mouse Ndufs4-/- and WT soleus muscles","INSTITUTE":"North-West University","LAST_NAME":"Louw","FIRST_NAME":"Roan","ADDRESS":"Hofman Street","EMAIL":"Roan.Louw@nwu.ac.za","PHONE":"+27 18 299 4074"},

"SUBJECT":{"SUBJECT_TYPE":"Mammal","SUBJECT_SPECIES":"Mus musculus","TAXONOMY_ID":"10090","GENOTYPE_STRAIN":"Ndufs4, https://www.jax.org/strai n/02705 8","AGE_OR_AGE_RANGE":"45-50 days","GENDER":"Male","ANIMAL_ANIMAL_SUPPLIER":"Jackson Laboratory (ME, USA)","ANIMAL_LIGHT_CYCLE":"12:12 h","ANIMAL_FEED":"Rodent Breeder, Cat. #RM1845, LabChef, Nutritionhub","ANIMAL_WATER":"ad libitum"},
"SUBJECT_SAMPLE_FACTORS":[
{
"Subject ID":"-",
"Sample ID":"Ms_1",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_3",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_6",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_7",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_9",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_11",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_13",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_15",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_16",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_18",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_20",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_22",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_25",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_27",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_28",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_30",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_31",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_32",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_33",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_36",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_39",
"Factors":{"Genotype":"WT"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_2",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_4",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_5",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_8",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_10",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_12",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_14",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_17",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_19",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_21",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_23",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_24",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_26",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_29",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_34",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_35",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_37",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_38",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
},
{
"Subject ID":"-",
"Sample ID":"Ms_40",
"Factors":{"Genotype":"Ndufs4-/-"},
"Additional sample data":{"Muscle type":"Soleus"}
}
],
"COLLECTION":{"COLLECTION_SUMMARY":"Mice were euthanized between postnatal day (P) 45-50 via cervical dislocation at the same time of day (8:00-9:00 AM) after overnight (12-h) fasting. From both hind limbs, white muscle portions of quadriceps femoris, as well as soleus muscles were collected. Tissues were snap-frozen in liquid nitrogen (within 15 min post-mortem) and stored at -80°C until used.","SAMPLE_TYPE":"Muscle"},

"TREATMENT":{"TREATMENT_SUMMARY":"The animals did not receive any treatment"},

"SAMPLEPREP":{"SAMPLEPREP_SUMMARY":"Muscle tissues were finely minced and homogenized in the presence of internal standards using a vibration mill. Metabolite extraction was achieved using a modified monophasic Bligh–Dyer extraction method with a solvent ratio of 3:1:1 (methanol:water:chloroform)."},

"CHROMATOGRAPHY":{"CHROMATOGRAPHY_TYPE":"Reversed phase","INSTRUMENT_NAME":"Agilent 1200","COLUMN_NAME":"Agilent C18 Zorbax SB-AQ (150 x 2.1mm, 3.5um)"},

"ANALYSIS":{"ANALYSIS_TYPE":"MS"},

"MS":{"MS_COMMENTS":"-","INSTRUMENT_NAME":"Agilent 6410 QQQ","INSTRUMENT_TYPE":"Triple quadrupole","MS_TYPE":"ESI","ION_MODE":"POSITIVE"},

"MS_METABOLITE_DATA":{
"Units":"Normalized peak area",

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"Metabolites":[{"Metabolite":"Taurine","PubChem ID":"1123"},{"Metabolite":"Ornithine","PubChem ID":"6262"},{"Metabolite":"3-Methylhistidine","PubChem ID":"64969"},{"Metabolite":"Histidine","PubChem ID":"6274"},{"Metabolite":"Lysine","PubChem ID":"5962"},{"Metabolite":"1-Methylhistidine","PubChem ID":"7020397"},{"Metabolite":"Arginine","PubChem ID":"28782"},{"Metabolite":"Glycine","PubChem ID":"5257127"},{"Metabolite":"Asparagine","PubChem ID":"6267"},{"Metabolite":"Serine","PubChem ID":"5951"},{"Metabolite":"Glutamine","PubChem ID":"5961"},{"Metabolite":"Beta-Alanine","PubChem ID":"239"},{"Metabolite":"Dimethylglycine","PubChem ID":"673"},{"Metabolite":"Threonine","PubChem ID":"6288"},{"Metabolite":"cis-4-hydroxyproline","PubChem ID":"440015"},{"Metabolite":"Alanine","PubChem ID":"5950"},{"Metabolite":"Citrulline","PubChem ID":"6992098"},{"Metabolite":"Betaine","PubChem ID":"247"},{"Metabolite":"Gamma-Aminobutyric acid","PubChem ID":"119"},{"Metabolite":"Carnitine","PubChem ID":"10917"},{"Metabolite":"Proline","PubChem ID":"145742"},{"Metabolite":"Creatine","PubChem ID":"586"},{"Metabolite":"Pipecolic acid","PubChem ID":"25200477"},{"Metabolite":"Valine","PubChem ID":"6287"},{"Metabolite":"Methionine","PubChem ID":"5255805"},{"Metabolite":"CAR(2:0)","PubChem ID":"10917"},{"Metabolite":"Tyrosine","PubChem ID":"6057"},{"Metabolite":"Leu-Ile","PubChem ID":"435718"},{"Metabolite":"CAR(3:0)","PubChem ID":"10917"},{"Metabolite":"Pyroglutamic acid","PubChem ID":"7405"},{"Metabolite":"Phenylalanine","PubChem ID":"6140"},{"Metabolite":"Aspartic acid","PubChem ID":"70701347"},{"Metabolite":"CAR(4:0)","PubChem ID":"264"},{"Metabolite":"Tryptophan","PubChem ID":"6305"},{"Metabolite":"Glutamic acid","PubChem ID":"33032"},{"Metabolite":"Aminoadipic acid","PubChem ID":"469"},{"Metabolite":"CAR(4:0(3Me))","PubChem ID":"6426851"},{"Metabolite":"CAR(6:0)","PubChem ID":"10917"},{"Metabolite":"CAR(8:0)","PubChem ID":"379"},{"Metabolite":"N-Acetylaspartic acid","PubChem ID":"65065"},{"Metabolite":"N-acetylglutamic acid","PubChem ID":"70914"},{"Metabolite":"CAR(12:0)","PubChem ID":"168381"},{"Metabolite":"CAR(14:0)","PubChem ID":"11005"},{"Metabolite":"CAR(16:0)","PubChem ID":"11953816"},{"Metabolite":"CAR(18:0)","PubChem ID":"10917"}]
}

}