Data for (Study ST002709)
(Analysis AN004391)Values for each metabolite have been scaled by dividing by the mean across all factors Run Hierarchial cluster analysis on this study | Run Heatmap cluster analysis on this studyMetabolite | F1 | F2 | F3 | F4 | F5 | F6 | F7 | F8 |
---|---|---|---|---|---|---|---|---|
1-methylnicotinamide | 0.8404 | 1.7095 | 1.1005 | 1.4542 | 0.6547 | 0.5186 | 0.5265 | 1.1956 |
3-hydroxy-trimethyllysine | 1.0836 | 1.2260 | 0.9327 | 0.8617 | 1.0890 | 0.9142 | 0.6915 | 1.2014 |
4-aminobutyrate | 0.9500 | 1.1571 | 0.7849 | 1.0100 | 1.0769 | 0.9563 | 0.7257 | 1.3392 |
5^-methylthioadenosine | 0.8595 | 1.3297 | 0.7844 | 1.1155 | 0.9409 | 0.9723 | 0.7064 | 1.2914 |
6-phosphogluconic acid | 0.8967 | 0.9554 | 0.6773 | 0.5275 | 1.8959 | 0.9082 | 0.9165 | 1.2224 |
acetyl-carnitine | 0.8771 | 0.9231 | 0.9626 | 0.8946 | 1.0361 | 1.0880 | 1.1393 | 1.0792 |
acetyl-CoA | 1.0013 | 1.2473 | 0.8247 | 0.8231 | 1.3174 | 0.9713 | 0.7412 | 1.0737 |
adenylosuccinic acid | 0.3026 | 0.5131 | 0.2039 | 0.2654 | 2.4099 | 1.6280 | 0.9550 | 1.7221 |
ADP | 1.0501 | 1.2518 | 0.7704 | 0.8054 | 1.2281 | 0.9980 | 0.6978 | 1.1983 |
AICAR | 0.3406 | 3.3481 | 1.0637 | 1.8812 | 0.4594 | 0.2645 | 0.1443 | 0.4983 |
AIR | 0.1416 | 0.1519 | 0.1121 | 0.1750 | 2.2660 | 1.5731 | 1.0459 | 2.5344 |
alanine | 0.9216 | 1.0826 | 0.8968 | 0.8168 | 1.0579 | 1.1706 | 0.9271 | 1.1265 |
alpha-ketoglutarate | 1.0596 | 1.6316 | 0.9729 | 1.3714 | 0.5549 | 0.8074 | 0.4429 | 1.1593 |
AMP | 0.9478 | 1.2400 | 0.7905 | 0.8508 | 1.1880 | 1.0797 | 0.7700 | 1.1333 |
arachidic acid | 0.9266 | 1.2163 | 0.8772 | 0.7311 | 1.1740 | 0.9035 | 1.0010 | 1.1703 |
arginine | 0.8730 | 1.0563 | 0.7580 | 0.8538 | 1.2665 | 1.1436 | 1.0051 | 1.0437 |
argininosuccinate | 0.1725 | 0.2188 | 0.1216 | 0.1053 | 2.4325 | 1.9169 | 1.2728 | 1.7596 |
ascorbate | 2.1454 | 2.7087 | 1.1821 | 1.2786 | 0.2365 | 0.1897 | 0.1120 | 0.1470 |
asparagine | 0.1794 | 0.2143 | 0.1518 | 2.4821 | 0.3584 | 0.2980 | 0.2491 | 4.0669 |
aspartate | 1.7674 | 1.9737 | 1.3286 | 1.1463 | 0.6062 | 0.4149 | 0.3603 | 0.4026 |
ATP | 0.9902 | 1.4205 | 0.8614 | 0.8143 | 1.2414 | 0.8878 | 0.5987 | 1.1856 |
betaine | 1.3183 | 1.3526 | 1.2379 | 1.1344 | 0.7991 | 0.7052 | 0.6763 | 0.7762 |
CAIR | NA | 1.8337 | 0.1712 | 0.8845 | NA | 1.2770 | 0.2442 | 1.5893 |
carbamoyl-aspartate | 1.7716 | 1.8697 | 1.3629 | 1.3620 | 0.4385 | 0.4138 | 0.3379 | 0.4435 |
carnitine | 1.3883 | 1.6496 | 1.2082 | 1.1773 | 0.6709 | 0.6268 | 0.5146 | 0.7644 |
CDP | 1.0143 | 1.4101 | 0.8128 | 0.8126 | 1.2213 | 0.9351 | 0.6341 | 1.1597 |
CDP-choline | 1.3192 | 1.2938 | 0.6881 | 0.6504 | 1.4827 | 1.0000 | 0.5399 | 1.0258 |
CDP-ethanolamine | 1.7234 | 2.0002 | 0.5550 | 0.7886 | 0.9454 | 0.9157 | 0.2958 | 0.7758 |
choline | 1.3739 | 0.8833 | 0.5234 | 1.1065 | 1.3931 | 0.7511 | 0.6661 | 1.3026 |
cis-aconitate | 1.3917 | 1.8140 | 1.2578 | 1.3029 | 0.4552 | 0.5368 | 0.2967 | 0.9448 |
citrate / isocitrate | 1.2658 | 1.6634 | 1.1285 | 1.1707 | 0.6831 | 0.6600 | 0.3487 | 1.0799 |
CMP | 0.9188 | 1.0989 | 0.6640 | 0.7854 | 1.2469 | 1.1969 | 0.7827 | 1.3064 |
CoA | 0.6886 | 1.5477 | 0.8180 | 0.8790 | 0.7390 | 1.1578 | 0.7376 | 1.4323 |
creatine | 1.1680 | 1.1865 | 1.0651 | 1.1844 | 0.8284 | 0.7878 | 0.7418 | 1.0381 |
creatinine | 0.9920 | 1.2602 | 1.0149 | 1.0319 | 0.9501 | 0.9353 | 0.8471 | 0.9685 |
CTP | 1.0546 | 1.5987 | 0.8068 | 0.8067 | 1.2403 | 0.7810 | 0.5169 | 1.1951 |
cystathionine | 0.7322 | 0.5902 | 0.6354 | NA | 1.0444 | 0.6247 | 1.1135 | 1.6322 |
cysteine | 0.1849 | NA | NA | 0.4371 | 0.5274 | NA | 0.1471 | 3.7035 |
cysteine-glutathione disulfide | 2.6413 | 0.1514 | 0.5713 | 0.1256 | 3.1214 | 0.1649 | 1.0664 | 0.1577 |
cystine | 1.9954 | NA | 0.3549 | 0.0494 | 1.8818 | 0.1071 | 0.6800 | NA |
cytidine | 1.1788 | NA | NA | NA | 0.7318 | NA | NA | NA |
dAMP | 1.3015 | NA | NA | NA | 0.6985 | NA | NA | NA |
dATP | 1.2400 | 1.6693 | 0.6895 | 0.9280 | 1.2099 | 0.8044 | 0.4414 | 1.0175 |
dCTP | 0.8860 | 1.9540 | 1.0684 | 0.6730 | 1.1528 | 0.7595 | 0.5754 | 0.9309 |
dihydroorotate | 1.8307 | 2.0350 | 1.3561 | 1.1663 | 0.4939 | 0.3936 | 0.3456 | 0.3788 |
dihydroxyacetone-phosphate | 0.7721 | 1.1088 | 0.7071 | 0.7371 | 1.2020 | 1.7802 | 0.7992 | 0.8934 |
dTMP | 0.2959 | 2.3542 | 0.6992 | 1.1365 | 0.3746 | 1.2407 | 0.6148 | 1.2842 |
dTTP | 1.1774 | 1.5937 | 0.8159 | 0.8232 | 1.1920 | 0.8314 | 0.5032 | 1.0633 |
FAICAR | 0.3522 | 0.6839 | NA | 0.4843 | 1.8571 | 1.2372 | 1.0039 | 1.2107 |
FGAM | 0.0881 | 0.1126 | 0.0523 | 0.0830 | 2.8941 | 1.5211 | 0.8825 | 2.3662 |
FGAR | 0.2501 | 0.6661 | 0.3495 | 0.3624 | 1.6446 | 1.7375 | 1.0293 | 1.9605 |
folate | 0.9682 | 1.3399 | 0.4278 | 0.9629 | 1.4440 | 1.2356 | 0.5669 | 1.0547 |
fructose | 0.9272 | 1.1314 | 1.0056 | 0.7544 | 1.0809 | 1.0344 | 0.9666 | 1.0994 |
fructose-1;6-bisphosphate | 0.8151 | 1.3168 | 0.6316 | 0.7540 | 1.3912 | 1.0891 | 0.6708 | 1.3313 |
fructose-1-phosphate | 1.5345 | 2.1240 | 0.3687 | 1.3582 | 0.9774 | 0.6791 | 0.0986 | 0.8595 |
fructose-6-phosphate | 0.8459 | 1.0492 | 0.7856 | 0.6516 | 1.3013 | 1.1633 | 0.8884 | 1.3147 |
fumarate | 0.3538 | 0.4369 | 0.2693 | 0.2510 | 1.9459 | 1.6492 | 1.2758 | 1.8181 |
gamma-butyrobetaine | 1.2240 | 1.4565 | 1.1720 | 1.1438 | 0.7786 | 0.7296 | 0.6615 | 0.8340 |
gamma-glutamylcysteine | 2.1360 | 0.5108 | 1.8181 | 0.6269 | 1.0917 | 0.4056 | 0.6852 | 0.7255 |
GAR | NA | 1.8975 | 0.3101 | 1.1515 | 0.8733 | 0.4410 | 0.6571 | 1.2110 |
GDP | 0.8440 | 1.1373 | 0.6802 | 0.6868 | 1.5090 | 1.0634 | 0.7198 | 1.3595 |
glucose | 0.9182 | 1.1526 | 1.0122 | 0.7556 | 1.1550 | 1.0220 | 1.1792 | 0.8053 |
glucose-6-phosphate | 0.9166 | 1.1812 | 0.8364 | 0.7263 | 1.2429 | 0.9636 | 0.9450 | 1.1880 |
glutamate | 0.9458 | 1.1986 | 0.8125 | 0.9300 | 1.0936 | 1.0132 | 0.7764 | 1.2299 |
glutamine | 0.7371 | 0.8783 | 0.5752 | 0.6633 | 1.6029 | 1.2830 | 0.9751 | 1.2851 |
glyceraldehyde-3-phosphate | 0.6806 | 0.8274 | 0.4988 | 0.5535 | 1.7415 | 1.2672 | 0.8559 | 1.5752 |
glycerol-3-phosphate | 0.8612 | 1.4482 | 0.7826 | 0.9135 | 1.1148 | 1.0428 | 0.7090 | 1.1278 |
glycerophosphocholine | 0.8078 | 0.9398 | 0.7255 | 0.7253 | 1.2900 | 1.2070 | 1.0550 | 1.2496 |
glycine | 0.5052 | 0.9638 | 0.5457 | 0.6298 | 1.8266 | 1.3693 | 1.0251 | 1.1344 |
GMP | 0.7447 | 0.9595 | 0.6022 | 0.6737 | 1.3829 | 1.3742 | 0.8666 | 1.3963 |
GSH | 1.0051 | 1.0062 | 0.8546 | 0.7131 | 1.3411 | 0.9691 | 0.9096 | 1.2013 |
GSSG | 1.1719 | 0.6593 | 0.7590 | 0.4366 | 2.3979 | 0.7705 | 0.9863 | 0.8185 |
GTP | 0.7859 | 1.2735 | 0.6546 | 0.6421 | 1.6157 | 0.9670 | 0.6277 | 1.4335 |
guanosine | 1.0569 | 1.2753 | 0.6719 | 0.8998 | 1.3386 | 1.0948 | 0.4956 | 1.1671 |
histidine | 0.9172 | 1.0560 | 0.7122 | 0.7700 | 1.5370 | 1.0943 | 0.8759 | 1.0374 |
hydroxyglutarate | 1.4009 | 1.8901 | 1.1366 | 1.5885 | 0.3918 | 0.5059 | 0.2892 | 0.7969 |
hypotaurine | 0.8046 | 0.9603 | 0.6944 | 0.6244 | 1.4374 | 1.1967 | 0.9709 | 1.3114 |
imidazoleacetic acid | 0.8638 | 1.3332 | 0.9465 | 1.0116 | 0.8554 | 1.0799 | 0.7869 | 1.1226 |
IMP | 0.3378 | 0.4811 | 0.2683 | 0.3569 | 2.2957 | 1.4239 | 0.8883 | 1.9478 |
kynurenic acid | 0.9965 | 1.0459 | 1.4248 | 0.6695 | 0.6893 | 0.6018 | 1.9859 | 0.5864 |
kynurenine | 0.5063 | 0.5108 | 1.5747 | 0.4024 | 0.9857 | 0.7928 | 2.5489 | 0.6785 |
L-2-aminobutyric acid | 1.1131 | 1.1596 | 0.9306 | 1.0045 | 1.1231 | 0.9725 | 0.6232 | 1.0734 |
lactate | 1.1151 | 0.9513 | 0.8135 | 0.9635 | 1.2042 | 0.9317 | 1.0167 | 1.0040 |
lauric acid | 1.2512 | 1.1065 | 0.6447 | 0.7388 | 1.3325 | 0.8524 | 0.8156 | 1.2584 |
leucine / isoleucine | 0.8528 | 0.8663 | 0.6160 | 0.6688 | 1.5893 | 1.2028 | 1.0320 | 1.1720 |
lysine | 0.8609 | 1.0713 | 0.6809 | 0.8042 | 1.3927 | 1.1793 | 0.9708 | 1.0401 |
malate | 1.7560 | 2.0470 | 1.4538 | 1.5443 | 0.3330 | 0.2831 | 0.2093 | 0.3735 |
methionine | 0.8724 | 0.9004 | 0.4000 | 0.7469 | 1.6261 | 1.4163 | 0.7171 | 1.3208 |
methioninesulfoxide | 0.2112 | 0.3365 | 2.3992 | 0.2351 | 0.5309 | 0.3668 | 3.5825 | 0.3378 |
myristic acid | 1.2357 | 1.2163 | 0.7587 | 0.7412 | 1.0264 | 0.6736 | 0.8400 | 1.5082 |
N-acetylglucosamine-phosphate | 2.4568 | 0.7111 | 0.1885 | 0.4042 | 2.5472 | 0.7355 | 0.1880 | 0.7687 |
N-acetylglutamate | 1.1333 | 1.2554 | 0.7155 | 0.9656 | 1.2600 | 0.9321 | 0.5237 | 1.2144 |
NAD+ | 0.9527 | 1.2123 | 0.8699 | 0.8364 | 1.1879 | 0.9862 | 0.8538 | 1.1009 |
NADH | 0.8732 | 1.0086 | 0.7726 | 0.8076 | 1.0047 | 1.1977 | 0.8364 | 1.4993 |
NADP+ | 0.8757 | 1.2148 | 0.7544 | 0.7855 | 1.2617 | 1.0396 | 0.7592 | 1.3090 |
nicotinamide | 0.9590 | 1.1100 | 0.8218 | 0.8671 | 1.2767 | 1.0560 | 0.9367 | 0.9727 |
N-trimethyllysine | 0.6267 | 0.7647 | 0.5163 | 0.5654 | 1.6270 | 1.4040 | 1.0889 | 1.4071 |
oleic acid | 2.8083 | 0.3579 | 0.2284 | 0.2060 | 3.5450 | 0.2895 | 0.2450 | 0.3199 |
ornithine | 0.8920 | 0.8906 | 0.7318 | 0.8108 | 1.3040 | 1.2227 | 1.1986 | 0.9495 |
orotate | 1.6852 | 1.6972 | 1.4846 | 1.0196 | 0.5861 | 0.6321 | 0.3468 | 0.5484 |
palmitic acid | 1.1173 | 1.2250 | 0.7389 | 0.7546 | 1.0548 | 0.7714 | 0.9251 | 1.4129 |
phenylalanine | 0.8207 | 0.7917 | 0.6363 | 0.7010 | 1.4962 | 1.2873 | 1.1201 | 1.1468 |
phosphate | 0.9547 | 1.1770 | 0.8449 | 0.9274 | 1.1411 | 1.0470 | 0.9050 | 1.0029 |
phosphatidylethanolamine | 1.2254 | 1.6595 | 0.7059 | 1.2291 | 1.0744 | 0.6537 | 0.3637 | 1.0883 |
phosphocholine | 0.9961 | 1.0741 | 0.9129 | 0.9261 | 1.0955 | 1.0011 | 0.9191 | 1.0751 |
phosphocreatine | 0.9649 | 1.3378 | 0.9498 | 0.8257 | 1.0298 | 0.9860 | 0.7745 | 1.1316 |
phosphoenolpyruvate | 1.1440 | 1.4936 | 0.8841 | 0.8465 | 1.1000 | 0.9544 | 0.6044 | 0.9729 |
phosphoglycerate | 1.2423 | 1.5365 | 0.8436 | 0.9374 | 1.1249 | 0.7306 | 0.4871 | 1.0975 |
phosphoribosylamine | 0.7628 | 0.7199 | 0.4961 | 0.4813 | 2.5687 | 0.8123 | 0.8388 | 1.3201 |
phosphorylethanolamine | 0.9713 | 1.4008 | 0.8812 | 0.8988 | 1.1429 | 0.9096 | 0.7020 | 1.0936 |
phosphoserine | 0.4953 | 0.6205 | 0.3634 | 0.3511 | 2.4318 | 1.3580 | 1.1697 | 1.2103 |
proline | 1.7959 | 1.7991 | 1.3871 | 1.7029 | 0.3713 | 0.3004 | 0.2446 | 0.3987 |
propionyl-carnitine | 1.4493 | 1.4652 | 1.2985 | 0.8607 | 0.7713 | 0.8081 | 0.6634 | 0.6837 |
PRPP | 0.5310 | 1.5135 | 0.6146 | 0.5921 | 1.1914 | 1.1396 | 0.5613 | 1.8565 |
pyruvate | 0.8668 | 1.1409 | 0.7612 | 0.9738 | 0.7505 | 1.5285 | 1.0458 | 0.9327 |
quinolinic acid | 0.9480 | 0.6502 | 0.6533 | 0.9881 | 1.4010 | 1.1926 | 1.2841 | 0.8828 |
riboflavin | 1.0268 | 1.2967 | 0.3258 | 0.9919 | 1.5851 | 1.3523 | 0.4834 | 0.9380 |
rib/ribul/xylul-ose-phosphate | 0.6850 | 0.6236 | 0.3514 | 0.3226 | 2.7246 | 1.2386 | 0.7439 | 1.3103 |
S-(1;2-Dicarboxyethyl)glutathione | 0.2076 | 0.3052 | 0.1741 | 0.1637 | 2.0782 | 1.8251 | 1.2678 | 1.9784 |
S-(2-Succinyl)-L-cysteine | 0.4183 | 0.2467 | 0.2930 | 0.1597 | 2.8016 | 1.1640 | 1.6164 | 1.3002 |
saccharopine | 0.2387 | 0.3473 | 0.1987 | 0.2787 | 1.6359 | 1.6601 | 0.8309 | 2.8097 |
S-adenosyl-homocysteine | 0.8236 | 1.2967 | 0.8958 | 0.8885 | 0.9396 | 1.0568 | 0.9419 | 1.1570 |
S-adenosyl-methionine | 0.8991 | 1.1774 | 0.7141 | 0.9824 | 0.9821 | 1.2186 | 0.8265 | 1.1997 |
SAICAR | 0.1153 | 0.3075 | 0.1360 | 0.1440 | 2.6280 | 1.8619 | 1.1331 | 1.6742 |
sarcosine | 0.8910 | 1.0154 | 0.9056 | 0.8494 | 1.0996 | 1.0545 | 1.0374 | 1.1472 |
sedoheptulose-7-phosphate | 0.7295 | 0.9122 | 0.5508 | 0.6190 | 1.6046 | 1.1762 | 0.9678 | 1.4399 |
serine | 0.5934 | 0.7050 | 0.4724 | 0.5368 | 1.6865 | 1.4996 | 1.1428 | 1.3634 |
sorbitol | 0.7574 | 1.0761 | 0.9205 | 0.6522 | 1.1866 | 1.1182 | 1.0553 | 1.2337 |
stearic acid | NA | 1.2346 | 0.9017 | 0.8313 | NA | 0.8560 | 0.8687 | 1.3076 |
succinate | 0.6904 | 0.7879 | 0.5091 | 0.4776 | 1.7791 | 1.4666 | 1.1084 | 1.1809 |
taurine | 0.9141 | 1.0323 | 0.8462 | 0.8015 | 1.2385 | 1.0797 | 0.9969 | 1.0908 |
threonine | 0.8139 | 0.8801 | 0.6191 | 0.6677 | 1.5716 | 1.2712 | 1.0226 | 1.1537 |
trifluoromethanesulfonate | 0.9545 | 1.2345 | 0.8385 | 0.8096 | 1.2019 | 1.0225 | 0.7918 | 1.1467 |
tryptophan | 0.8073 | 0.9639 | 0.4131 | 0.6794 | 1.7297 | 1.3796 | 0.7319 | 1.2951 |
tyrosine | 0.7308 | 0.8846 | 0.5391 | 0.6271 | 1.6732 | 1.3074 | 0.9732 | 1.2646 |
UDP | 1.0945 | 1.5560 | 0.8638 | 0.8550 | 1.1667 | 0.8253 | 0.5325 | 1.1062 |
UDP-glucuronic acid | 1.0000 | 1.4294 | 0.8114 | 0.7795 | 1.2479 | 0.9003 | 0.6441 | 1.1874 |
UDP-N-acetylglucosamine | 1.0510 | 1.3016 | 0.8119 | 0.7415 | 1.1767 | 1.0134 | 0.7298 | 1.1740 |
UMP | 0.9398 | 1.2116 | 0.7595 | 0.7987 | 1.1934 | 1.1299 | 0.7736 | 1.1935 |
uric acid | 1.7237 | 1.1422 | 0.8837 | 0.4836 | 0.9662 | 1.2159 | 0.9342 | 0.6505 |
urocanic acid | 1.1879 | 0.9150 | 1.1796 | 1.3633 | 1.0989 | 0.6394 | 0.7174 | 0.8985 |
UTP | 1.1023 | 1.5907 | 0.9118 | 0.8696 | 1.1735 | 0.7498 | 0.4951 | 1.1073 |
valine | 0.8774 | 0.7964 | 0.6715 | 0.7934 | 1.4466 | 1.1370 | 1.1313 | 1.1465 |
XMP | 0.6955 | 1.0849 | 0.2662 | 0.7121 | 1.6748 | 1.3801 | 0.5232 | 1.4186 |
xylonic acid | 1.2376 | 1.5703 | 0.9408 | 0.9028 | 1.0441 | 0.6612 | 0.7350 | 0.9081 |
xylulose | 0.8444 | 0.9101 | 0.4069 | 0.6539 | 1.6560 | 1.4647 | 0.7073 | 1.3566 |
Factors:
F1 | Genotype:FH | Tracers used:3,3,3',3'-D4 Cystine |
F2 | Genotype:FH | Tracers used:none |
F3 | Genotype:FH | Tracers used:U-C13 glucose |
F4 | Genotype:FH | Tracers used:U-C13 glutamine |
F5 | Genotype:WT | Tracers used:3,3,3',3'-D4 Cystine |
F6 | Genotype:WT | Tracers used:none |
F7 | Genotype:WT | Tracers used:U-C13 glucose |
F8 | Genotype:WT | Tracers used:U-C13 glutamine |