MGP Database

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MGP000902

Ontology/Pathway Information

Entrez Gene ID1892
Gene Nameenoyl CoA hydratase, short chain, 1, mitochondrial
Gene Symbol ECHS1
SpeciesHomo sapiens
Gene Ontology (GO Annotations)
GO IDSourceTypeDescription
GO:0070062 IDA:UniProtKBCextracellular vesicular exosome
GO:0005759 TAS:ReactomeCmitochondrial matrix
GO:0005739 TAS:UniProtKBCmitochondrion
GO:0004300 TAS:ReactomeFenoyl-CoA hydratase activity
GO:0044255 TAS:ReactomePcellular lipid metabolic process
GO:0006635 TAS:ReactomePfatty acid beta-oxidation
GO:0044281 TAS:ReactomePsmall molecule metabolic process
REACTOME Pathway Links
REACTOME Pathway IDDescription
REACT_419Beta oxidation of butanoyl-CoA to acetyl-CoA
REACT_1708Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
REACT_1887Beta oxidation of hexanoyl-CoA to butanoyl-CoA
REACT_735Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
REACT_1697Beta oxidation of octanoyl-CoA to hexanoyl-CoA
REACT_22279Fatty acid, triacylglycerol, and ketone body metabolism
REACT_111217Metabolism
REACT_22258Metabolism of lipids and lipoproteins
REACT_1473Mitochondrial Fatty Acid Beta-Oxidation
REACT_1541mitochondrial fatty acid beta-oxidation of saturated fatty acids
SMP Pathway Links
SMP IDDescription
SMP007192-aminoadipic 2-oxoadipic aciduria
SMP001372-Methyl-3-Hydroxybutryl CoA Dehydrogenase Deficiency
SMP001383-Hydroxy-3-Methylglutaryl-CoA Lyase Deficiency
SMP005213-hydroxyisobutyric acid dehydrogenase deficiency
SMP005223-hydroxyisobutyric aciduria
SMP002373-Methylcrotonyl Coa Carboxylase Deficiency Type I
SMP001393-Methylglutaconic Aciduria Type I
SMP001403-Methylglutaconic Aciduria Type III
SMP001413-Methylglutaconic Aciduria Type IV
SMP00173Beta-Ketothiolase Deficiency
SMP00073Butyrate Metabolism
SMP00538Carnitine palmitoyl transferase deficiency (I)
SMP00541Carnitine palmitoyl transferase deficiency (II)
SMP00181Ethylmalonic Encephalopathy
SMP00054Fatty Acid Elongation In Mitochondria
SMP00051Fatty acid Metabolism
SMP00185Glutaric Aciduria Type I
SMP00186Glutaric Aciduria Type III
SMP00527Hyperlysinemia I, Familial
SMP00528Hyperlysinemia II or Saccharopinuria
SMP00523Isobutyryl-coa dehydrogenase deficiency
SMP00524Isovaleric acidemia
SMP00238Isovaleric Aciduria
SMP00544Long-chain-3-hydroxyacyl-coa dehydrogenase deficiency (LCHAD)
SMP00539Long chain acyl-CoA dehydrogenase deficiency (LCAD)
SMP00037Lysine Degradation
SMP00198Malonic Aciduria
SMP00502Malonyl-coa decarboxylase deficiency
SMP00199Maple Syrup Urine Disease
SMP00542Medium chain acyl-coa dehydrogenase deficiency (MCAD)
SMP00384Methylmalonate Semialdehyde Dehydrogenase Deficiency
SMP00200Methylmalonic Aciduria
SMP00201Methylmalonic Aciduria Due to Cobalamin-Related Disorders
SMP00482Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
SMP00481Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
SMP00480Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
SMP00016Propanoate Metabolism
SMP00236Propionic Acidemia
SMP00571Pyridoxine dependency with seizures
SMP00239Saccharopinuria/Hyperlysinemia II
SMP00568Short-chain 3-hydroxyacyl-CoA dehydrogenase deficiency (SCHAD)
SMP00235Short Chain Acyl CoA Dehydrogenase Deficiency (SCAD Deficiency)
SMP00545Trifunctional protein deficiency
SMP00032Valine, Leucine and Isoleucine Degradation
SMP00540Very-long-chain acyl coa dehydrogenase deficiency (VLCAD)
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